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The Journal of Pediatrics
Volume 156, Issue 5
, Pages 823-827
, May 2010
Long-Term Treatment of Cystinosis in Children with Twice-Daily Cysteamine
References
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- . The effects of cysteamine on the upper gastrointestinal tract of children with cystinosis. Pediatr Nephrol. 1997;11:600–603
- . Feeding problems in cystinosis. Pediatr Nephrol. 1998;12:365–370
- . The evaluation and treatment of gastrointestinal disease in children with cystinosis receiving cysteamine. J Pediatr. 2003;143:224–230
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- Understanding intestinal cysteamine bitartrate absorption. J Pediatr. 2006;148:764–769
- . Cystinosis: intracellular cystine depletion by aminothiols in vitro and in vivo. J Clin Invest. 1976;58:180–189
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- . Cystine-binding protein assay for cystine. Methods Enzymol. 1987;143:144–148
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- . A simultaneous liquid chromatography/mass spectrometric assay of glutathione, cysteine, homocysteine and their disulfides in biological samples. J Pharmaceut Biomed Anal. 2003;31:251–261
- . A unified approach to mixed linear models. Am Stat. 1991;45:54–63
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- . A simple estimate of glomerular filtration rate in children derived from body length and plasm creatinine. Pediatrics. 1976;58:259–263
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Supported by the Cystinosis Research Foundation (Irvine, CA) and the National Institutes of Health (grant MO1RR00827). The authors declare no conflicts of interest.
PII: S0022-3476(09)01194-9
doi: 10.1016/j.jpeds.2009.11.059
© 2010 Mosby, Inc. All rights reserved.
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The Journal of Pediatrics
Volume 156, Issue 5
, Pages 823-827
, May 2010
