« Previous
Next »
The Journal of Pediatrics
Volume 153, Issue 6
, Pages 752-757
, December 2008
Improvements in Lung Function Outcomes in Children with Cystic Fibrosis are Associated with Better Nutrition, Fewer Chronic Pseudomonas aeruginosa Infections, and Dornase Alfa Use
References
- . Prediction of mortality in patients with cystic fibrosis. N Engl J Med. 1992;326:1187–1191
- . Predictive 5-year survivorship model of cystic fibrosis. Am J Epidemiol. 2001;153:345–352
- . Longitudinal analysis of pulmonary function decline in patients with cystic fibrosis. J Pediatr. 1997;131:809–814
- . Risk of death in cystic fibrosis patients with severely compromised lung function. Chest. 1998;113:1230–1234
- . Patient registry 2006: annual data report. http://www.cff.orgAccessed
- . Improving rate of decline of FEV1 in young adults with cystic fibrosis. Thorax. 2006;61:155–157
- . Identifying treatments that halt progression of pulmonary disease in cystic fibrosis. Pediatr Res. 1997;41:161–165
- Risk factors for rate of decline in forced expiratory volume in one second in children and adolescents with cystic fibrosis. J Pediatr. 2007;151:134–139
- . Standardization of spirometry: 1994 update. Am J Respir Crit Care Med. 1995;152:1107–1136
- Standardisation of spirometry. Eur Respir J. 2005;26:319–338
- Pulmonary function between 6 and 18 years of age. Pediatr Pulmonol. 1993;15:75–78
- . Physical growth: National Center for Health Statistics percentiles. Am J Clin Nutr. 1979;32:607–629
- . Trends in pulmonary function in patients with cystic fibrosis correlate with the degree of glucose intolerance at baseline. Am J Respir Crit Care Med. 2000;162:891–895
- Predictors of deterioration of lung function in cystic fibrosis. Pediatr Pulmonol. 2002;33:483–491
- Acceleration of lung disease in children with cystic fibrosis after Pseudomonas aeruginosa acquisition. Pediatr Pulmonol. 2001;32:277–287
- . Clinical use of ibuprofen is associated with slower FEV1decline in children with cystic fibrosis. Am J Respir Crit Care Med. 2007;176:1084–1089
- . Annual lung function changes in young patients with chronic lung disease. Eur Respir J. 2002;19:886–891
- Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis. N Engl J Med. 1994;331:637–642
- A two-year randomized, placebo-controlled trial of dornase alpha in young patients with cystic fibrosis with mild lung function abnormalities. J Pediatr. 2001;139:813–820
- Infant care patterns at epidemiologic study of cystic fibrosis sites that achieve superior childhood lung function. Pediatrics. 2007;119:e531–e537
- . Longitudinal relationship among growth, nutritional status, and pulmonary function in children with cystic fibrosis: analysis of the Cystic Fibrosis Foundation National CF Patient Registry. J Pediatr. 2000;137:374–380
- Growth and nutritional indexes in early life predict pulmonary function in cystic fibrosis. J Pediatr. 2003;142:624–630
- . DNA concentrations in BAL fluid of cystic fibrosis patients with early lung disease: influence of treatment with dornase alpha. Pediatr Pulmonol. 2005;39:1–4
The authors have no conflicts of interest to disclose. There was no sponsor involvement in the design of this study or in the preparation of this manuscript for publication.
PII: S0022-3476(08)00591-X
doi: 10.1016/j.jpeds.2008.07.011
© 2008 Mosby, Inc. All rights reserved.
« Previous
Next »
The Journal of Pediatrics
Volume 153, Issue 6
, Pages 752-757
, December 2008
